Decoding Hemophilia: Understanding ICD-10 Codes For This Rare Bleeding Disorder

What is ICD-10 for Hemophilia?

Hemophilia is a rare genetic disorder that impairs the body’s ability to control blood clotting. It is a lifelong condition that can lead to excessive bleeding and bruising. The ICD-10 code for hemophilia is D66.

Code Information

ALPROLIX® Professional Site  Hemophilia B Resources
ALPROLIX® Professional Site Hemophilia B Resources

The ICD-10 code D66 is used to classify hemophilia into different types, such as hemophilia A, hemophilia B, and other forms of the disorder. This code helps healthcare providers accurately diagnose and treat patients with hemophilia.

Diagnostic Related Groups (MS-DRG)

Coagulation Disorders: Hereditary and Hemorrhagic Disorders
Coagulation Disorders: Hereditary and Hemorrhagic Disorders

In the Medicare Severity-Diagnosis Related Group (MS-DRG) system, hemophilia is classified under DRG 810, which includes cases of coagulation disorders. This DRG helps determine the reimbursement rates for hospitals treating patients with hemophilia.

Convert to ICD-9 Code

ICD--CM Diagnosis Code D
ICD–CM Diagnosis Code D

For those still using the ICD-9 code system, the equivalent code for hemophilia in ICD-9 is 286.0. This code is used to indicate various forms of hemophilia, similar to the classifications in ICD-10.

Code History

The ICD-10 code for hemophilia has undergone several revisions over the years to ensure accurate classification and coding for this genetic disorder. Healthcare providers must stay up-to-date with the latest changes to properly document and treat patients with hemophilia.

Approximate Synonyms

Some approximate synonyms for hemophilia in ICD-10 include Hemorrhagic disorder due to intrinsic circulating anticoagulants and Hereditary factor VIII deficiency disease. These terms are used interchangeably with hemophilia to describe the same condition.

Clinical Information

Hemophilia is caused by a deficiency or dysfunction of clotting factors in the blood, specifically factor VIII (hemophilia A) or factor IX (hemophilia B). This leads to prolonged bleeding and difficulty forming blood clots, which can result in serious complications if not properly managed.


Hemophilia is an inherited genetic disorder that is passed down from parent to child. It primarily affects males, as the faulty gene responsible for hemophilia is located on the X chromosome. Females can be carriers of the gene but are typically not affected by the disorder.


The symptoms of hemophilia can vary depending on the severity of the condition. Common signs include easy bruising, prolonged bleeding from minor cuts or injuries, and joint pain or swelling. Severe cases of hemophilia can lead to spontaneous bleeding or internal bleeding, which can be life-threatening.


Diagnosing hemophilia involves a series of blood tests to measure clotting factors and determine the type and severity of the disorder. Medical history and family history are also important factors in diagnosing hemophilia, as it is a genetic condition that runs in families.


Treatment for hemophilia typically involves replacing the missing clotting factor through intravenous infusions. This helps the blood clot more effectively and reduces the risk of bleeding. In severe cases, prophylactic treatment may be necessary to prevent bleeding episodes and maintain overall health.


In conclusion, understanding the ICD-10 code for hemophilia is essential for accurate diagnosis and treatment of this genetic disorder. Healthcare providers must be familiar with the various classifications and synonyms for hemophilia to effectively document and code cases. Proper management and treatment can improve the quality of life for patients with hemophilia and reduce the risk of complications.


1. What are the different types of hemophilia classified in ICD-10?
2. How is hemophilia diagnosed in patients?
3. What are the treatment options for hemophilia?
4. Can females be affected by hemophilia?
5. How does the ICD-10 code for hemophilia impact reimbursement rates for healthcare providers?

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