Unraveling The Mystery Of Primary Myelofibrosis: Understanding ICD-10 Coding

What is Primary Myelofibrosis ICD 10?

Primary Myelofibrosis is a rare type of chronic blood cancer that affects the bone marrow. It is classified under the ICD-10 code D47.1. This condition causes the bone marrow to become scarred and fibrotic, leading to a decrease in the production of normal blood cells.

Code Information

Pathology Outlines - Primary myelofibrosis
Pathology Outlines – Primary myelofibrosis

The ICD-10 code for Primary Myelofibrosis is D47.1. This code is used to classify and report cases of this specific type of blood cancer in medical records and billing systems.

Diagnostic Related Groups (MS-DRG)

ICD--CM Diagnosis Code D
ICD–CM Diagnosis Code D

Primary Myelofibrosis falls under MS-DRG 813 – Coagulation Disorders. This DRG grouping is used for reimbursement purposes in hospitals and healthcare settings.

Convert to ICD-9 Code

Primary Myelofibrosis can be converted to the ICD-9 code 289.83. This code was used prior to the adoption of the ICD-10 coding system.

Code History

The ICD-10 code for Primary Myelofibrosis was introduced in 2015 as part of the transition from ICD-9 to ICD-10 coding systems. It replaced the previous ICD-9 code 289.83.

Approximate Synonyms

Other terms that may be used to describe Primary Myelofibrosis include Idiopathic Myelofibrosis, Agnogenic Myeloid Metaplasia, and Myelosclerosis with Myeloid Metaplasia.

Clinical Information

Primary Myelofibrosis is a chronic and progressive disease that primarily affects older adults. It is characterized by the abnormal proliferation of blood cells in the bone marrow, leading to fibrosis and scarring of the marrow tissue.


The exact cause of Primary Myelofibrosis is unknown. However, it is thought to be related to genetic mutations that affect the production and function of blood cells in the bone marrow.


Common symptoms of Primary Myelofibrosis include fatigue, weakness, pale skin, easy bruising, enlarged spleen, and bone pain. Some patients may also experience fever, night sweats, and weight loss.


Primary Myelofibrosis is diagnosed through a combination of medical history, physical examination, blood tests, bone marrow biopsy, and imaging studies. Genetic testing may also be performed to identify specific mutations associated with the disease.


Treatment for Primary Myelofibrosis focuses on managing symptoms, reducing complications, and improving quality of life. Options may include medication, blood transfusions, stem cell transplantation, and supportive care. Clinical trials and experimental therapies may also be considered for some patients.


Primary Myelofibrosis is a complex and challenging blood disorder that requires careful management and treatment by a team of healthcare professionals. Early diagnosis and intervention can help improve outcomes and quality of life for patients living with this condition.


1. What is the prognosis for patients with Primary Myelofibrosis?
2. Can Primary Myelofibrosis be cured?
3. What are the risk factors for developing Primary Myelofibrosis?
4. How is Primary Myelofibrosis different from other types of myeloproliferative disorders?
5. Are there any lifestyle changes that can help manage Primary Myelofibrosis?

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