Wegener’s Disease: Understanding The ICD-10 Classification

What is Wegener’s Disease ICD 10?

Wegener’s disease, also known as granulomatosis with polyangiitis (GPA), is a rare autoimmune disorder that causes inflammation of the blood vessels in the nose, sinuses, throat, lungs, and kidneys. It is characterized by the formation of granulomas, which are small clusters of cells that can cause damage to tissues and organs.

Code Information

The ICD-10 code for Wegener’s disease is M31.30. This code is used to classify and assign a specific code to this rare autoimmune disorder for medical billing and diagnostic purposes.

Diagnostic Related Groups (MS-DRG)

PDF] Accuracy of the ICD- Code for Identification of Patients
PDF] Accuracy of the ICD- Code for Identification of Patients

Wegener’s disease falls under MS-DRG 682 – Renal Failure with MCC (Major Complications or Comorbidities). This DRG is used to classify patients who have renal failure as a result of Wegener’s disease and require significant medical intervention and treatment.

Convert to ICD-9 Code

In the past, Wegener’s disease was classified under the ICD-9 code 446.4. However, with the implementation of ICD-10 coding system, the new code M31.30 is now used to identify and classify this autoimmune disorder.

Code History

ICD--CM Diagnosis Code M
ICD–CM Diagnosis Code M

The ICD-10 code M31.30 for Wegener’s disease was introduced in October 2015 as part of the updated coding system to provide more specific and accurate codes for various medical conditions and diseases.

Approximate Synonyms

Other names for Wegener’s disease include granulomatosis with polyangiitis (GPA) and Wegener’s granulomatosis. These terms are often used interchangeably to refer to the same autoimmune disorder.

Clinical Information

Wegener’s disease is characterized by inflammation of the blood vessels, which can lead to damage of various organs and tissues in the body. Common symptoms include sinus pain, nosebleeds, coughing up blood, and kidney problems.


The exact cause of Wegener’s disease is unknown, but it is believed to be triggered by an abnormal immune response that causes inflammation of the blood vessels. Genetic factors and environmental triggers may also play a role in the development of this autoimmune disorder.


Some common symptoms of Wegener’s disease include persistent sinus pain, nosebleeds, coughing up blood, chest pain, shortness of breath, joint pain, and kidney problems. If left untreated, Wegener’s disease can lead to serious complications and organ damage.


Diagnosing Wegener’s disease can be challenging, as the symptoms are similar to other respiratory and autoimmune disorders. Medical history, physical examination, blood tests, imaging studies, and biopsy of affected tissues are often used to confirm the diagnosis of Wegener’s disease.


Treatment for Wegener’s disease typically involves a combination of corticosteroids, immunosuppressant medications, and other medications to control inflammation and suppress the abnormal immune response. In severe cases, surgery may be needed to repair damaged organs or tissues.


In conclusion, Wegener’s disease is a rare autoimmune disorder that causes inflammation of the blood vessels and can lead to serious complications if left untreated. Proper diagnosis and treatment are essential to manage symptoms and prevent organ damage in patients with Wegener’s disease.


1. What are the risk factors for developing Wegener’s disease?

Some risk factors for Wegener’s disease include genetic predisposition, exposure to certain environmental triggers, and a history of other autoimmune disorders.

2. Is Wegener’s disease curable?

While there is no cure for Wegener’s disease, early diagnosis and treatment can help manage symptoms and prevent complications in patients with this autoimmune disorder.

3. Can Wegener’s disease affect children?

Wegener’s disease is rare in children, but it can occur in individuals of any age. Children with Wegener’s disease may experience similar symptoms as adults and require specialized medical care.

4. Are there any lifestyle changes that can help manage Wegener’s disease?

Managing Wegener’s disease involves following a healthy lifestyle, including a balanced diet, regular exercise, and avoiding smoking and exposure

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